Gambaran Karakteristik Penyakit Hirschsprung di RSUD Al-Ihsan Bandung Periode 1 Januari 2016 - 30 September 2019

Sylvia Agustina Maidah, Ismet Mucthar Nur, Dicky Santosa

Abstract


Abtract. Hirschprung’s disease is a disease that caused by underdeveloped enteric nervesmarked by the absence of ganglion cells in the myenteric plexus and submucosaof distal intestine. In the newborn, Hirschprung’s disease often comes withsymptomsof vomiting, abdominal distension, and difficulty to remove themeconium in 24 hours after birth. The most common compicatons and should be watched out for Hirschsprung’s disease are usually enterocolitis, intestinal perforasi and sepsis which are the most common causes of death. This study used descriptive method. Thepurpose of this study is to find the description and characteristic of Hirschprung’sdisease patient based on diagnosed age, clinical symptoms, and location ofaganglionic segment in Al Ihsan Regional Public Hospital Bandung from Januari 1 st 2016 – September 30 th 2019. The data result comes from medical records. Themethod is total sampling, obtained 53 medical records within inclusive criteria.The most common characteristic based on clinical symptoms are bloating andconstipation (39.6%), age are 1-2 years old (39.6%), and aganglionic segment isrectum (100%). Patients with Hirschprung’s disease are widely reported at 1-2years old and the most common location is rectum. The clinical symptoms thatoften underlie the patient’s parents to bring their children to get treatment arebloating and constipation. This research needs to be followed up on Hirschsprung’s disease in a greater number of causes, especially in detecting significant symptoms, an through evaluating every action taken.

Keywords: Hirschsprung Disease, Clinical Symptoms, Diagnosed Age, Location of Aganglionic Segment

 

Abstrak. Penyakit Hirschsprung merupakan penyakit yang timbul akibat tidak berkembangnya saraf enterik yang ditandai dengan tidak terdapatnya sel-sel ganglion di pleksus myenterik dan submukosa pada usus bagian distal. Pada periode bayi baru lahir, penyakit Hirschsprung sering datang dengan gejala muntah-muntah, distensi abdomen, dan susah untuk mengeluarkan meconium selama 24 jam setelah kelahiran. Komplikasi yang paling sering terjadi dan harus diwaspadai akibat penyakit Hirschsprung biasanya enterocolitis, perforasi usus dan sepsis yang merupakan penyebab kematian tersering.Penelitian ini merupakan penelitian deskriftif bertujuan untuk mengetahui gambaran karakteristik Penyakit Hirschsprung berdasarkan usia terdiagnosis, gejala klinis dan letak segmen aganglionik di RSUD Al-Ihsan Bandung periode 1 januari 2016 – 30 september 2019. Sampel  data berupa rekam medis, dengan cara total sampling  didapatkan 53 rekam medisyang memenuhi kriteria inklusi. Gambaran gejala klinis yang sering muncul terbanyak adalah perut kembung dan sulit BAB (39,6%), usia terbanyak adalah 1-2 tahun (39,6%), letak segmen aganglionik terbanyak adalah rectum (100,0%). Penderita Hirschsprung Disease banyak dilaporkan di usia 1-2 tahun dan lokasi terbanyak di rektum. Gejala klinis yang paling sering mendasari orang tua penderita membawa anaknya berobat yaitu perut kembung dan sulit buang air besar. Penelitian ini perlu dilakukan tindak lanjutan terhadap penyakit hirschsprung dalam jumlah  kasus lebih besar, khususnya dalam mendeteksi gejala yang signifikan, serta melakukan evaluasi terhadap setiap tindakan yang dilakukan.

Kata Kunci: Hirschsprung Disease, Gejala Klinis, Usia Terdiagnosis, Letak Segmen Aganglionik


Keywords


Hirschsprung Disease, Gejala Klinis, Usia Terdiagnosis, Letak Segmen Aganglionik

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DOI: http://dx.doi.org/10.29313/kedokteran.v0i0.21483

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